Title | Concomittant fibrous dysplasia with aneurysmal bone cyst formation within the skull, humerus and rib. |
Publication Type | Journal Article |
Year of Publication | 2018 |
Authors | Kaloostian SW, Vartanian TK, Ordookhanian C, Vartanian T, Kaloostian PE |
Journal | J Surg Case Rep |
Volume | 2018 |
Issue | 7 |
Pagination | rjy180 |
Date Published | 2018 Jul |
ISSN | 2042-8812 |
Abstract | Polyostotic fibrous dysplasia (FD) is a rare pathology characterized by the abnormal and gradual replacement of normal bone (calcium hydroxylapatite of osteoid matrix) with fibrous connective tissue. Aneurysmal bone cyst (ABC) is a tumor-like benign lesion with blood-filled cavities that can affect virtually any bone in the body. We report on a 20-year-old male presenting with an extremely rare pathology of FD with ABC formation of the skull, fourth rib and humerus. Our case report represents a novel literary addition to rare FD with ABC pathologies. Optimal diagnosis of this rare pathology can be achieved by a full body evaluation for clinical and radiographic FD with or without ABC, and optimal treatment for this rare pathology is the maximum surgical excision of the tumor and/or soft tissue. |
DOI | 10.1093/jscr/rjy180 |
Alternate Journal | J Surg Case Rep |
PubMed ID | 30057744 |
PubMed Central ID | PMC6055640 |